Ectopia cordis fetal ultrasound

Ectopia cordis results from the failure of lateral mesoderm migration into the midline. Some forms may be the outcome of amniotic band syndrome 11.The four main ectopic positions are:adjacent to the thorax: ~60%abdominal: 15-30%thoracoabdominal: 7-18% cervical: ~3%AssociationsEctopia cordis may occur as an isolated malformation or associated with a larger category of ventral body wall defects that affect the thorax, abdomen, or both.Individual associationsVentricular septal defect and tetralogy of Fallot are the most common intracardiac defects. Omphalocele is the most common abdominal wall defect.Syndromic associationsA well-known association is pentalogy of Cantrell, which comprises of 1:ectopia cordisomphalocele (typically supraumbilical)congenital diaphragmatic herniasternal cleftcongenital heart disease